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020 _a3319501682
_q(electronic bk.)
020 _a9783319501680
_q(electronic bk.)
020 _z3319501666
020 _z9783319501666
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050 4 _aRC845
_b2017 EB
245 0 0 _aBiliary disease :
_bfrom science to clinic
_cGideon Hirschfield, David Adams, Evaggelia Liaskou, editors.
264 1 _aCham, Switzerland
_bSpringer International Publishing
_c2017
264 4 _c2017
300 _a1 recurso en línea
_bilustraciones (algunas a color)
336 _aTexto
_btxt
_2rdacontent
337 _aelectrónico
_bc
_2rdamedia
338 _arecurso electrónico
_bcr
_2rdacarrier
347 _atext file
_bPDF
_2rda
504 _aIncluye referencias bibliográficas
505 0 _aPreface; Contents; 1: The Clinical Burden of€Biliary Disease: A€Global Perspective; 1.1 Pediatric Cholestatic Disorders; 1.2 Extrahepatic Biliary Atresia; 1.3 Progressive Familial Intrahepatic Cholestatic Syndromes; 1.4 Drug-Induced Cholestasis; 1.5 Primary Biliary Cholangitis; 1.6 Primary Sclerosing Cholangitis; 1.7 Autoimmune Sclerosing Cholangitis/IgG4 Cholangiopathy; 1.8 Cholangiocarcinoma; 1.9 Gallbladder Cancer; 1.10 Gallstone Disease; References; 2: The Healthy Biliary Tree: Cellular and€Immune Biology; 2.1 The Normal Biliary Tree; 2.2 Development of€the€Bile Duct Epithelium.
505 8 _a2.2.1 Morphogens and€Transcription Factors Involved in€Biliary Lineage Specification and€Bile Duct Formation2.3 Biological Properties Enabling Cholangiocytes to€Respond to€Liver Damage; 2.3.1 Reactive Ductular Cells: The€Main Element of€the€Hepatic Response to€Damage; 2.3.2 Cholangiocyte Proliferation; 2.3.3 Cholangiocyte Role in€Bile Secretion; 2.3.4 Cholangiocytes in€Inflammation; 2.3.5 Cholangiocytes and€Innate Immunity; 2.3.5.1 TLR Signaling; 2.3.5.2 Cholangiocyte Secretion of€IgA and€Antimicrobial Peptides; 2.3.6 Cholangiocyte Involvement in€Antigen Presentation; References.
505 8 _a3.2.3 Vascular Diseases Associated with€Bile Duct Injury3.2.3.1 Hepatic Arterial Occlusion ("Ischaemic Cholangiopathy"); 3.2.3.2 "Sclerosing Cholangitis in€Critically Ill Patients" (SC-CIP); 3.2.3.3 Portal Vein Occlusion ("Portal Hypertensive Biliopathy"); 3.2.4 Infective Causes of€Biliary Disease; 3.2.5 Drugs and€Iatrogenic Causes of€Biliary Disease; 3.2.5.1 Drug-Induced Cholestasis; 3.2.5.2 Intestinal Failure-Associated Liver Disease (IFALD); 3.2.6 Neoplastic Diseases Associated with€Cholestasis or Bile Duct Injury; 3.2.6.1 Langerhans Cell Histiocytosis.
505 8 _a3: Pathological Features of€Biliary Disease in€Children and€Adults3.1 What Are the€Pathological Features of€Biliary Disease?; 3.1.1 Bile Duct Lesions; 3.1.2 Ductular Reaction; 3.1.3 Cholestasis; 3.1.3.1 Bilirubinostasis; 3.1.3.2 Cholate Stasis; 3.1.4 Inflammation; 3.1.5 Fibrosis; 3.1.6 Assessment of€Disease Severity in€Chronic Biliary Disease: Grading and€Staging; 3.2 Histological Changes in€Specific Diseases; 3.2.1 Developmental/Genetic Diseases; 3.2.1.1 Biliary Atresia; 3.2.1.2 Syndromic and€Non-syndromic Paucity of€Intrahepatic Bile Ducts.
505 8 _aSyndromic Paucity of€Intrahepatic Bile Ducts (Alagille Syndrome)Non-syndromic Paucity of€Intrahepatic Bile Ducts; 3.2.1.3 Diseases Associated with€Ductal Plate Malformation; 3.2.1.4 Cystic Fibrosis; 3.2.1.5 Progressive Familial Intrahepatic Cholestasis (PFIC); 3.2.2 Immune-Mediated Biliary Diseases; 3.2.2.1 Primary Biliary Cholangitis (PBC); 3.2.2.2 Primary Sclerosing Cholangitis (PSC); 3.2.2.3 Autoimmune Sclerosing Cholangitis (ASC); 3.2.2.4 IgG4-Associated Sclerosing Cholangitis; 3.2.2.5 Sarcoidosis; 3.2.2.6 Transplant-Related Bile Duct Diseases.
520 3 _aThis book addresses the current understanding of the diagnosis and management of biliary disease across all ages, with emphasis on how the latest advances in clinical science may be integrated into current and future therapies. The coverage is wide ranging, encompassing congenital and acquired conditions including cholestatic syndromes, biliary atresia, drug-induced cholestasis, primary biliary cholangitis/cirrhosis, primary sclerosing cholangitis, cholangiocarcinoma, gallstone disease, and autoimmune sclerosing cholangitis. With contributions from basic and clinical scientists, the relevance of state-of-the-art mechanistic biology to diagnosis, treatment, and future opportunities for drug design is clearly explained. The balance between science and clinical practice will ensure that this book makes a lasting contribution to the field. A broad readership will find the book easy to access and a rich source of information on current best practice and evolving management strategies.
650 7 _aVías biliares
_xEnfermedades
_2embne
_0(OCoLC)fst00831716
_0
_9677697
700 1 _aAdams, David,
_d1958-
_eeditor literario
700 1 _aHirschfield, Gideon M.,
_eeditor literario
700 1 _aLiaskou, Evaggelia,
_eeditor literario
856 4 0 _uhttps://go.openathens.net/redirector/universidadeuropea.es?url=http://link.springer.com/10.1007/978-3-319-50168-0
_zAcceso a este recurso digital (usuarios Universidad Europea de Madrid)
988 _aSpringer_Medicine_2017
998 _b02/2018
_dz
_e-
_zSI
999 _c95462
_d95462
_x1