000 02371nam a22003255i 4500
001 75839
003 ES-MaUEC
005 20230202101747.0
007 cr nn 008mamaa
008 120917s2013 xxu| s |||| 0|eng d
020 _a9781461437222
040 _aES-MaUEC
050 4 _aRB147.5
_b.M58 2013 EB
245 0 0 _aMitochondrial Disorders Caused by Nuclear Genes
_cedited by Lee-Jun C. Wong.
260 _aNew York
_bSpringer International Publishing
_c2013
300 _a1 recurso en línea (XII, 369 p.) 32 il., 20 il. col.
336 _aTexto (visual)
_btxt
_2rdacontent
337 _aelectrónico
_bc
_2rdamedia
338 _arecurso electrónico
_bcr
_2rdacarrier
520 _aMitochondrial cytopathies are mutations in the inherited maternal mitochondrial genome, or the nuclear DNA-mutation. Mitochondrial respiratory chain disorders (RCD) are a group of genetically and clinically heterogeneous diseases, due to the fact that protein components of the respiratory chain are encoded by both mitochondrial and nuclear genomes and are essential in all cells.Â{u026E} addition, the biogenesis, structure and function of mitochondria, including DNA replication, transcription, and translation, all require nuclear encoded genes.Â{u04E9}nce mitochondria are present in every cell, every tissue, mitochondrial disorders usually affects multiple organs. Mitochondrial Disorders Caused by Nuclear Genes discusses the biochemical, molecular, clinical, and genetic aspects of complex dual genome mitochondrial disorders. Chapters include genes involved in mitochondrial DNA biogenesis and maintenance of mitochondrial DNA integrity, complex subunits and assembly genes, and mitochondrial protein translation related diseases.
942 _2lcc
_cLE
988 _aEBOOK, EBSPRINGERrevisado
650 0 7 _aPatología mitocondrial
_2embne
_9414723
700 1 _aWong, Lee-Jun C.
_eeditor
_984509
_0Local
856 4 0 _uhttps://go.openathens.net/redirector/universidadeuropea.es?url=https://link.springer.com/book/10.1007/978-1-4614-3722-2
_zAcceso a este recurso digital (usuarios Universidad Europea de Madrid)
901 _ai9781461437222
907 _a.b1281457x
_b10-10-17
_c01-10-14
998 _am
_a_alco
_a_vill
_b22-03-17
_cm
_dz
_eu
_feng
_gxxu
_h0
945 _aRB147.5 .M58 2013 EB
_g1
_ieBOOK
_j0
_lmae
_o-
_pEUR0.00
_q-
_r-
_sb
_t15
_u0
_v0
_w0
_x0
_y.i11543954
_z06-04-17
999 _c75839
_d75839
_x1