000 03018nam a22002895i 4500
001 402893
003 ES-MaUEC
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008 231227s2023 sz | o |||| 0|eng d
020 _a9783031431562
024 7 _a10.1007/978-3-031-43156-2
_2doi
040 _aES-MaUEC
_bspa
_cES-MaUEC
_dES-MaUEC
050 4 _aRC633-647
_b2023 EB
245 0 0 _aCongenital Bleeding Disorders :
_bDiagnosis and Management
_cedited by Akbar Dorgalaleh
250 _a2nd ed. 2023
264 1 _aCham
_bSpringer International Publishing
_c2023
300 _a1 recurso en línea
336 _atexto
_btxt
_2rdacontent
337 _aelectrónico
_bc
_2rdamedia
338 _arecurso electrónico
_bcr
_2rdacarrier
505 0 _a An Overview of Hemostasis -- Congenital Bleeding Disorders: Diagnosis and Management -- von Willebrand disease: an update on diagnosis and treatment -- Hemophilia A, Diagnosis and Management -- Hemophilia B, Diagnosis and Management -- Congenital fibrinogen disorders, diagnosis, and management -- Congenital Prothrombin Deficiency: Diagnosis and Management -- Congenital Factor V Deficiency -- Combined Factor V and Factor VIII Deficiency, Diagnosis and Management -- Congenital Factor VII Deficiency, Diagnosis and Management -- Vitamin K-dependent Coagulation Factors Deficiency, Diagnosis and Management -- Congenital Factor X deficiency, Diagnosis and Management -- Congenital Factor XI Deficiency -- Congenital Factor XIII Deficiency, Diagnosis and Management -- Glanzmann Thrombasthenia -- Bernard-Soulier Syndrome, Diagnosis and Management -- Gray Platelet Syndrome (GPS). .
520 _aThis significantly updated new edition describes in detail the clinical presentations, diagnosis, and management of a wide range of congenital bleeding disorders. It will assist readers in overcoming the significant challenges involved in clinical and laboratory diagnosis and in providing effective clinical care that makes optimal use of new products, including recombinant factor concentrate. The coverage ranges from hemophilia A and B and von Willebrand disease to rare bleeding disorders such as congenital factor V, factor X, factor XI, and factor XIII deficiency and inherited platelet function disorders. The exceptional attention to rarer conditions is of particular importance given the considerable risk of overlooking them during diagnosis, with potential consequences for disease-related morbidity and mortality. The authors are acknowledged specialists in the field from across the world who have particular expertise in the disorder that they discuss. The book will be of value tohematologists, oncologists, pediatricians, laboratory specialists and technicians, general physicians, and trainees.
856 4 0 _uhttps://go.openathens.net/redirector/universidadeuropea.es?url=https://doi.org/10.1007/978-3-031-43156-2
_zAcceso a este recurso digital (usuarios Universidad Europea de Madrid)
942 _2lcc
_cLE
988 _aSpringer_Medicine_2023
999 _c402893
_d402893