Preface 1 BehÃ{u00A7}et syndrome -- Preface 2 BehÃ{u00A7}et's syndrome: the role of patient's Associations -- The numbers of BehÃ{u00A7}et: a rare disease -- Along the Old Silk Road -- Epidemiology of BehÃ{u00A7}et's syndrome -- BehÃ{u00A7}et's syndrome according to classical and population genetics -- Infections, autoimmunity and BehÃ{u00A7}etâ€{u3833}yndrome: what liaison -- Pathogenesis of BehÃ{u00A7}et's syndrome -- Muco-cutaneous involvement in BehÃ{u00A7}et's syndrome -- Neurological and neuro-psychological manifestation in BehÃ{u00A7}et's syndrome -- Ocular involvement and BehÃ{u00A7}et -- Muscle and articular manifestations in BehÃ{u00A7}et's syndrome -- Cardiovascular issues -- Intestinal BehÃ{u00A7}et Disease -- Audio vestibular involvement in BehÃ{u00A7}et's disease -- Pregnancy and BehÃ{u00A7}et's syndrome -- Pediatric Onset of BehÃ{u00A7}et's syndrome -- Differential Diagnosis -- Classification and Diagnosis Criteria for BehÃ{u00A7}et's Disease -- Prognosis and Disease Activity -- Old and New Treatment for BehÃ{u00A7}et's Disease -- Surgical management of BehÃ{u00A7}et's Disease.

BehÃ{u00A7}et's syndrome can reasonably be considered a unique entity among diseases of the immune system for several reasons: It has specific features and, uniquely among the immune system pathologies, represents a link between autoimmune diseases, systemic vasculitis, and autoinflammatory diseases. In addition, it is of interest to a variety of specialists, including immunologists, rheumatologists, dermatologists, and ophthalmologists, and requires a complex multidisciplinary approach. Many aspects need to be considered in a syndrome that presents a wide spectrum of symptoms and for which the therapeutic armamentarium is expanding significantly, with the development of new treatments, not least the so-called biologics. This book offers comprehensive coverage of the disease by some of the worldâ€{u382C}eading experts in BehÃ{u00A7}et's syndrome from all the relevant specialties. Epidemiology, genetics, pathogenesis, organ system involvement, differential diagnosis, novel treatments, surgical management, and prognosis are just some of the topics addressed. BehÃ{u00A7}et's Syndrome: From Pathogenesis to Treatment will be an invaluable reference for a range of practitioners, researchers, and undergraduates or postgraduates interested in immunorheumatology, dermatology, and rare diseases.