Section I: general concepts 1. IntroductionClassification -- 2 Histopathology of IEM. Section II: Preoperative Evaluation: 3 ENT -- 4 Audiology -- 5 Radiology -- 6 Speech and Language Evaluation -- 7 Psychology.-8 Neurosurgery -- 9 Genetic evaluation. Section III: IEM management: 10 Genetics of IEM -- 11 Treatment Algorithm -- 12 CSF Fistula and meningitis -- 13 Facial nerve Abnormalities -- 14 Stapedotomy -- 15 CSF leakage and management -- 16 First Consensus Meeting -- 17 CI vs ABI in IEMs -- 18 ABI Surgery -- 19 Complete Labyrinthine Aplasia -- 20 Rudimentary Otocyst -- 21 Common Cavity -- 22 Cochlear Aplasia -- 23 IP-I -- 24 IP-II -- 25 IP-III -- 26 Cochlear Hypoplasia. -27 EVA ? -- 28 Cochlear Aperture Abnormalities -- 29 Cochlear Nerve Deficiency -- 30 Vestibular Malformations -- 31 Second Consensus Meeting -- 32 Audiological Outcome with CI -- 33 Audiological Outcome with ABI.

This book, built on the latest internationally recognized classification system to which the volume editor contributed, offers a unique and comprehensive reference guide to the clinical presentation, characteristics and proper treatment of the wide spectrum of congenital malformations of the inner ear (IEM). IEMs are common, accounting for roughly 20% of congenital hearing loss cases, and can be difficult to manage: 8 groups are identified, which are completely different from each other. With a wealth of color figures and extra videos, the book provides an in-depth description of all the relevant aspects: from histopathology assessment, to preoperative evaluation, genetics, different surgical and non-surgical options, and outcomes. The results from two international Consensus Pediatric Auditory Brainstem Implantation Meetings are also included. Written by leading experts in the field, this volume will be an invaluable and multidisciplinary tool for otolaryngologists, audiologists and radiologists, while also benefiting scientists dealing with genetics, and neurosurgeons dealing with brainstem implants.