Part 1. Entities without or little systemic implications -- 1. Autoinflammatory Keratinization Diseases -- 2. Adult Mucinoses: New And Revisited Variants -- 3. Pediatric Cutaneous Mucinoses -- 4. Circumscribed Palmoplantar Hypokeratosis -- 5. Necrotizing Infundibular Crystalline Folliculitis And Necrotizing Eosinophilic Folliculitis -- 6. Annular Erythema: New And Revisited Variants -- 7. Frontal Fibrosing Alopecia -- 8. Terra Firma-Forme Dermatosis And Dermatosis Neglecta -- 9. Papular Epidermal Nevus With "Skyline" Basal Cell Layer (PENS) -- 10. Grover Disease -- 11. The Spectrum Of Acquired Elastolytic Disorders -- 12. Post Irradiation Pseudo-Sclerodermatous Panniculitis -- 13. Linear Focal Elastosis And Pxe-Like Fibroelastolytic And Elastotic Papulosis Disorders -- 14. Rare Variants Of Keratosis Pilaris -- 15. Cutaneous Collagenous Vasculopathy -- 16. Acquired Hyperpigmentation Disorders Of Uncertain Etiology -- 17. Eruptive pseudoangiomatosis, eruptive hypomelanosis and paraviral exanthems -- 18.Morbihan Disease -- Part 2. Entities with systemic implications -- 19. Aquagenic Keratoderma -- 20. New Or Unusual Skin Manifestations In Monoclonal Gammopathies -- 21. Lipophagic/Lipoatrophic Panniculitis: A Th1 Mediated Autoimmune Disorder Of The Subcutaneous Fat -- 22. Covid19-Related Cutaneous Manifestations -- 23. PAPA, PASH, PAPASH, PsAPASH and PASS: autoinflammatory syndromes of Hidradenitis Suppurativa -- 24. Re-Emerging And New Skin Infections -- 25. Skin Adverse Reactions From New Cancer Immunotherapy -- 26. Newly Recognized Variants Of Neutrophilic Dermatosis -- 27. Cutaneous Reactive Angiomatoses -- 28. Skin Manifestations of Immunoglobulin G4-Related Disease -- 29. Necrolytic Acral Erythema (NAE) -- 30. Reactive Granulomatous Dermatitis (Interstitial granulomatous dermatitis, palisaded neutrophilic and granulomatous dermatitis, and variants) -- 31. Chronic Atypical Neutrophilic Dermatosis With Lipodystrophy And Elevated Temperature (CANDLE) and Proteasome Associated Autoinflammatory Syndrome (PRAAS) -- 32. Spiny Keratoderma -- 33. Cocaine-Levamisole-Induced Vasculitis/Vasculopathy Syndrome -- 34. Lymphocytic Thrombophilic Arteritis (Macular Lymphocytic Arteritis) -- 35. Dermal Hyperneury -- 36. Emergent cutaneous T-cell pseudolymphomas.

In recent years new, obscure or poorly known dermatological disorders have been described and better defined, with emphasis on clinical, histopathological and etiopathogenetic features. Familiarity with these new, emerging or revisited clinical entities is fundamental, and recognizing them with their differential diagnosis has important implications in clinical practice for better patient management. This book offers an in-depth discussion of the clinical and pathologic features of newly described or less well-known and revisited cutaneous disorders. It provides clinical findings, as well as the histologic, immunologic, and molecular features of these diseases in addition to therapeutic notes. The first section of the book covers cutaneous diseases that lack any systemic implications, such as circumscribed palmoplantar hypokeratosis, necrotizing infundibular crystalline folliculitis, and dermal hyperneury, amongst others. The second section offers coverage on cutaneous diseases with systemic implications, such as AESOP-POEMS syndrome, lipoatrophic panniculitis of children, and obesity associated with lymphedematous mucinosis. Each chapter describes an entity, along with an atlas of clinical manifestations that will serve as a "bed-side" clinical reference, followed by a series of photomicrographs depicting the histologic changes. Chapters also offer recent updates on molecular tools helpful in attaining the diagnosis as well as therapeutic recommendations based upon the more recent acquisitions. New and Emerging Entities in Dermatology and Dermatopathology is a must-have reference for the practicing dermatopathologist, internists, general pathologist reviewing skin biopsies, general dermatologists, family practitioners and nurse practitioners, geneticists, immunologists and other health care providers that care for patients with skin conditions.